Ameloblastoma is a rare tumor that usually appear on the jaw. This tumor is developed from cells that function to form tooth enamel, which also protect the teeth. It can cause pain and swelling, severely it may change the shape of the patient's face. If it continues to be left untreated, the tumor can become malignant and spread to the lymph nodes. The experts have not determined the cause of ameloblastoma but factors that are more sucpetible of developing this tumor. Patient who has experienced injury in the jaw and odontogenic infection have a risk of tumor development. Diagnosis is made based on radiological examinations and tumor tissue biopsy. Treatment that can be done to this case is surgery to remove the tumor. If the tumor has spread to other parts of the body, radiation therapy must be done after surgery. This case report explained what dentists can do as general practice when amelobastoma is found and what they should do.